Rabbit anti-PBE Antibody
Catalog #
PBE
Human
IP
,WB
Rabbit
Polyclonal
Whole IgG
between 673 and 723
IgG
Unconjugated
Antigen Affinity Purified
Product Details
Human
Human
2 - 8 °C
1 year from date of receipt
Peroxisomal bifunctional enzyme (PBE) is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of PBE contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in the PBE gene are a cause of peroxisomal disorders such as Zellweger syndrome [taken from NCBI Entrez Gene (Gene ID: 1962)].
Peroxisomal bifunctional enzyme
Alternate Names
3,2-trans-enoyl-CoA isomerase; 3-hydroxyacyl-CoA dehydrogenase; ECHD; Enoyl-CoA hydratase/3,2-trans-enoyl-CoA isomerase; enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase; enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenase; FRTS3; L-3-hydroxyacyl-CoA dehydrogenase; LBFP; L-bifunctional protein, peroxisomal; LBP; L-PBE; PBE; PBFE; peroxisomal bifunctional enzyme; peroxisomal enoyl-CoA hydratase
Applications