LRPPRC Antibody

LRPPRC is a leucine-rich protein that has multiple pentatricopeptide repeats (PPR). The precise role of this protein is unknown but studies suggest it may play a role in cytoskeletal organization, vesicular transport, or in transcriptional regulation of both nuclear and mitochondrial genes. The protein localizes primarily to mitochondria and is predicted to have an N-terminal mitochondrial targeting sequence. Mutations in this gene are associated with the French-Canadian type of Leigh syndrome [taken from NCBI Entrez Gene (Gene ID: 10128)].
LRPPRC
leucine rich pentatricopeptide repeat containing
Leucine-rich PPR motif-containing protein, mitochondrial
:  130 kDa leucine-rich protein CLONE-23970 GP130 Leigh syndrome, French-Canadian type (cytochrome oxidase deficiency) leucine-rich pentatricopeptide repeat containing leucine-rich PPR-motif containing LRP 130 LRP130 LSFC mitochondrial leucine-rich PPR motif-containing protein More... Less...
Product
Specifications
Ordering Information
Human
WB, IP, IHC
Between residue 1344 to 1394
$339
$229
$99