Peroxisomal bifunctional enzyme (PBE) is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of PBE contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in the PBE gene are a cause of peroxisomal disorders such as Zellweger syndrome [taken from NCBI Entrez Gene (Gene ID: 1962)].
Alternative names for
PBE Antibody include EHHADH antibody,
Peroxisomal bifunctional enzyme antibody,
enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase antibody,
peroxisomal bifunctional enzyme antibody,
3,2-trans-enoyl-CoA isomerase antibody,
peroxisomal enoyl-CoA hydratase antibody,
L-3-hydroxyacyl-CoA dehydrogenase antibody,
L-bifunctional protein, peroxisomal antibody,
enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenase antibody.