Peroxisomal bifunctional enzyme (PBE) is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of PBE contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in the PBE gene are a cause of peroxisomal disorders such as Zellweger syndrome [taken from NCBI Entrez Gene (Gene ID: 1962)].
Alternative names for
PBE Antibody include PBFE antibody, enoyl-CoA antibody, hydratase/3-hydroxyacyl CoA dehydrogenase antibody, EHHADH antibody, ECHD antibody, LBP antibody, LBFP antibody, L-PBE antibody.