PBE Antibody

Peroxisomal bifunctional enzyme (PBE) is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of PBE contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in the PBE gene are a cause of peroxisomal disorders such as Zellweger syndrome [taken from NCBI Entrez Gene (Gene ID: 1962)].
EHHADH
enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase
Peroxisomal bifunctional enzyme
:  3,2-trans-enoyl-CoA isomerase 3-hydroxyacyl-CoA dehydrogenase ECHD Enoyl-CoA hydratase/3,2-trans-enoyl-CoA isomerase enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenase FRTS3 L-3-hydroxyacyl-CoA dehydrogenase LBFP L-bifunctional protein, peroxisomal LBP L-PBE PBE PBFE peroxisomal enoyl-CoA hydratase More... Less...
Product
Specifications
Ordering Information
Human
WB, IP
Between 673 and 723
$339
$229
$99