BCKDE1A Antibody

BCKDE1A (branched chain keto acid dehydrogenase E1, alpha polypeptide) is a component of the branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex. The BCKD complex is an inner mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). Mutations in this gene result in maple syrup urine disease, type IA [taken from NCBI Entrez Gene (Gene ID: 593)].
BCKDHA
branched chain keto acid dehydrogenase E1, alpha polypeptide
2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
:  2-oxoisovalerate dehydrogenase (lipoamide) BCKDE1A BCKDH E1-alpha branched chain keto acid dehydrogenase E1 alpha protein branched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease) branched-chain alpha-keto acid dehydrogenase E1 component alpha chain maple syrup urine disease MSU MSUD1 OVD1A More... Less...
Product
Specifications
Ordering Information
Human
IP
Between 75 and 125
$339
$99
Human
WB, IP
Between 395 and 445
$339
$229
$99
Human
Includes: 1 each of A303-789A and A303-790A
$472
Includes: 1 each of A303-789A and A303-790A
Mouse
WB
Surrounding serine 293
This item is backordered. Please contact Bethyl Customer Support at 1-800-338-9579 if you are interested in purchasing this item. Expected Release mid January 2018 (Updated 10/19/2017)
$239
$99